Meng Z, Lin D, Wang G, et al. - A rare occurrence of congenital midureteral stenosis was documented among children studied, and this condition accounted for 1.6% of all ureteral obstructions. Its diagnosis is important and its management mainly involves resection of the stenotic segment and end-to-end ureteral anastomosis, with a good prognosis.

• In pediatric populations, midureteral stenosis occurs very rarely and can result in congenital hydronephrosis.

• This retrospective review involved 26 children diagnosed with congenital midureteral stenosis; of those 13 (50%) presented with prenatal hydronephrosis and the rest 13 (50%) complained of abdominal pain or a mass.

• A high diagnostic rate was obtained with urinary ultrasound, which should be the first choice for midureteral stenosis.

• In cases where diagnosis is challenging, retrograde pyelography can be employed but routine retrograde pyelography is not advised.

• Congenital ureteral stenosis has a relatively short lesion range, largely within 1 cm.

• Surgical management was adopted in all the cases.

• Participants underwent mean follow-up of 22 months (range: 6–50 months), and anastomotic strictures developed in one child, and relief of urinary tract obstruction was seen in the other children without long-term complications.