Alam S, Claxton JNS, Mortillo M, et al. - Comparison of survival of patients with Turner Syndrome and non-syndromic patients with similar left heart obstructive lesions (LHOLs) was performed.

• From the Pediatric Cardiac Care Consortium (PCCC), a US-based registry of CHS, 179 patients with TS operated for LHOL were identified: 161 with two-ventricle lesions (coarctation n = 149, aortic stenosis n = 12) and 18 with hypoplastic left heart (HLH) variants.

• Patients with TS and non-syndromic comparators with operated two-ventricle left heart obstructive lesions (LHOLs) were similar in terms of 30-year transplant-free survival; no excess congenital heart disease (CHD) risk was evident in those with TS.

• CVD morbidity, however, was still higher among patients with TS, emphasizing the relevance of lifelong comorbidity surveillance in this population.