This case study reviews the natural history and clinical and radiological characteristics of primary pediatric optic nerve sheath meningioma.

Study design

Researchers reviewed records from 8 pediatric patients with optic nerve sheath meningioma.

Outcomes

The mean age at presentation was 11 years (range 6–17 years). Each patient was followed between 71 to 297 months.

Two of the 8 patients had neurofibromatosis type 2. Six were observed, while 2 were treated with radiotherapy. Among the observed patients, 2 had minimal change in vision and did not experience tumor growth after long-term follow-up.

Limitations

The study was limited by its retrospective nature and small size.

Clinical significance

Optic nerve sheath meningiomas are very rare in the pediatric population, and, when they do occur, the diagnosis of neurofibromatosis should be considered. A subset of these tumors grow very slowly and can be managed conservatively with observation.